• 1  Cicardi M, Aberer W, Banerji A, et al. Classification, diagnosis and approach to treatment for angioedema: consensus report from the Hereditary Angioedema International Working Group. Allergy 2014;69:60216. Cross Ref link Pubmed link
  • 2  Zuraw BL. Hereditary angioedema. N Engl J Med 2008;359:102736. Cross Ref link Pubmed link
  • 3  Gompels MM, Lock RJ, Abinun M, et al. C1 inhibitor deficiency: consensus document. Clin Exp Immunol 2005;139:37994. Cross Ref link Pubmed link
  • 4  Leznoff A, Sussman GL. Syndrome of idiopathic chronic urticaria and angioedema with thyroid autoimmunity: a study in 90 patients. J Allergy Clin Immunol 1989;84:6671. Cross Ref link Pubmed link
  • 5  Massa MC, Connolly SM. An association between C1 esterase inhibitor deficiency and lupus erythematosus: report of two cases and review of literature. J Am Acad Dermatol 1982;7:25564. Cross Ref link Pubmed link
  • 6  Farkas H, Csuka D, Gács J, et al. Lack of increased prevalence of immunoregulatory disorders in hereditary angioedema due to C1‐inhibitor deficiency. Clin Immunol 2011;141:5866. Cross Ref link Pubmed link
  • 7  Bork K, Barnstedt SE, Koch P, Traupe H. Hereditary angioedema with normal C1‐inhibitor activity in women. Lancet 2000;356:21317. Cross Ref link Pubmed link
  • 8  Visy B, Füst G, Bygum A, et al. Helicobacter pylori infection as a triggering factor of attacks in patients with hereditary angioedema. Helicobacter 2007;12: 2517. Cross Ref link Pubmed link
  • 9  Bork K. Hereditary angioedema with normal C1 inhibitor activity including hereditary angioedema with coagulation factor XII gene mutations. Immunol Allergy Clin N Am 2006;26:70924. Cross Ref link
  • 10  Bork K, Fischer B, Dewald G. Recurrent episodes of skin angioedema and severe attacks of abdominal pain induced by oral contraceptives or hormone replacement therapy. Am J Med 2003;114:2948. Cross Ref link Pubmed link
  • 11  Agostoni A, Cicardi M. Hereditary and acquired C1‐inhibitor deficiency: biological and clinical characteristics in 235 patients. Medicine 1992;71:20615. Cross Ref link Pubmed link
  • 12  Williamson DM. Reticulate erythema: a prodrome in hereditary angio‐oedema. Br J Dermatol 1979;101:54952. Cross Ref link Pubmed link
  • 13  Bork K, Hardt J, Witzke G. Fatal laryngeal attacks and mortality in hereditary angioedema due to C1‐INH deficiency. J Allergy Clin Immunol 2012;130:6927. Cross Ref link Pubmed link
  • 14  Kapoor P, Greipp PT, Schaefer EW, et al. Idiopathic systemic capillary leak syndrome (Clarkson's disease): the Mayo clinic experience. Mayo Clin Proc 2010;85:90512. Cross Ref link Pubmed link
  • 15  Gleich GJ, Schroeter AL, Marcoux JP, et al. Episodic angioedema associated with eosinophilia. N Engl J Med 1984;310:16216. Cross Ref link Pubmed link
  • 16  Obuko Y, Sato E, Hossain M, et al. Periodic angioedema with eosinophilia: increased serum level of interleukin 5. Intern Med 1995;34:10811. Cross Ref link Pubmed link
  • 17  Tillie‐Leblond I, Gosset P, Janin A, et al. Increased interleukin‐6 production during the acute phase of the syndrome of episodic angioedema and hypereosinophilia. Clin Exp Allergy 1998;28:4916. Cross Ref link Pubmed link
  • 18  Weller K, Groffik A, Magerl M, et al. Development, validation and initial results of the angioedema activity acore (AAS). Allergy 2013; 68: 118592. Pubmed link
  • 19  Weller K, Groffik A, Magerl M, et al. Development and construct validation of the angioedema Quality of Life Questionnaire (AE‐QoL). Allergy 2012;67:128998. Cross Ref link Pubmed link
  • 20  Zuberbier T, Aberer W, Asero, et al. The EAACI/GA(2) LEN/EDF/WAO Guideline for the definition, classification, diagnosis, and management of urticaria: the 2013 revision and update. Allergy 2014;69:86887. Cross Ref link Pubmed link
  • 21  Choi G, Soeters MR, Farkas H, et al. Recombinant human C1‐inhibitor in the treatment of acute angioedema attacks. Transfusion 2007;47:102832. Cross Ref link Pubmed link
  • 22  Bork K, Frank J, Grundt B, et al. Treatment of acute edema attacks in hereditary angioedema with a bradykinin receptor‐2 antagonist (icatibant). J Allergy Clin Immunol 2007;119:1497503. Cross Ref link Pubmed link
  • 23  Schneider L, Lumry W, Vegh A, et al. Critical role of kallikrein in hereditary angioedema pathogenesis: a clinical trial of ecallantide, a novel kallikrein inhibitor. J Allergy Clin Immunol 2007;120:41622. Cross Ref link Pubmed link
  • 24  Bygum A, Vestergaard H. Acquired angioedema – occurrence, clinical features and associated disorders in a Danish nationwide patient cohort. Int Arch Allergy Immunol 2013;162:14955. Cross Ref link Pubmed link